하악에서 발생한 모세혈관확장형 골육종의 증례보고 및 문헌고찰
Telangiectatic Osteosarcoma of the Mandible: A Case Report and Review of Literature
이삭, 오규영, 윤혜정, 조성대, 이재일, 홍성두,
소속 상세정보
이삭 ( Lee Sak ) - Seoul National University School of Dentistry Department of Oral Pathology
오규영 ( Oh Kyu-Young ) - Seoul National University School of Dentistry Department of Oral Pathology
윤혜정 ( Yoon Hye-Jung ) - Seoul National University School of Dentistry Department of Oral Pathology
조성대 ( Cho Sung-Dae ) - Seoul National University School of Dentistry Department of Oral Pathology
이재일 ( Lee Jae-Il ) - Seoul National University School of Dentistry Department of Oral Pathology
홍성두 ( Hong Seong-Doo ) - Seoul National University School of Dentistry Department of Oral Pathology
Abstract
Telangiectatic osteosarcoma(TAEOS) is a rare subtype of osteosarcoma(OS) composed of blood-filled or empty cystic architecture simulating aneurysmal bone cyst. TAEOSs account for 2-12% of all OSs. TAEOSs mostly develop around knee and proximal humerus, but TAEOSs of the jaws are rare. To the best of my knowledge, this is the fourth case of primary TAEOS affecting the jaws. A 36-year-old female who had been previously diagnosed osteosarcoma by biopsy reported with a chief complaint of throbbing and swelling of the right mandible. The patient received neoadjuvant chemotherapy followed by hemi-mandibulectomy. After surgery, patient received adjuvant chemotherapy. The patient is free of disease for 6 months after surgery. TAEOSs are mimicking other benign entities, such as aneurysmal bone cyst and central giant cell granuloma. Thus, careful diagnosis through thorough radiographic and histopathologic evaluation is important to establish a treatment plan, prognosis, prediction and management strategy.
키워드
Telangiectatic osteosarcoma; Osteosarcoma; Mandible; Jaw
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